Congenital malformations of the inner ear are diverse. With the use of high-resolution CT and MRI, the diagnostic rate has improved significantly. The most common classification system is Sennaroglu classification, which categorizes malformations based on their location and severity into cochlear malformations, vestibular malformations, semicircular canal malformations, internal auditory canal malformations, and vestibular and cochlear aqueduct malformations.
Table 1 Sennaroglu classification of inner ear malformations
Clinically, the most common conditions are enlarged vestibular aqueduct and incomplete partition type II.
To be continued